- Decreased Myocyte Enhancer Factor 2 Levels in the Hippocampus of Huntington's Disease Mice Are Related to Cognitive Dysfunction.
- TBK1 phosphorylates mutant Huntingtin and suppresses its aggregation and toxicity in Huntington's disease models.
- Impaired intracellular trafficking of sodium-dependent vitamin C transporter 2 contributes to the redox imbalance in Huntington's disease.
- Editorial: Role of Protein Palmitoylation in Synaptic Plasticity and Neuronal Differentiation.
- DNA Methyltransferase 1 (DNMT1) Acts on Neurodegeneration by Modulating Proteostasis-Relevant Intracellular Processes.
- Mitochondrial Respiration Changes in R6/2 Huntington's Disease Model Mice during Aging in a Brain Region Specific Manner.
- Loss of Hap1 selectively promotes striatal degeneration in Huntington disease mice.
- Mitochondrial biology and the identification of biomarkers of Huntington's disease.
- Using Sigma-ligands as part of a multi-receptor approach to target diseases of the brain.
- Corrigendum to: Targeting Gpr52 lowers mutant HTT levels and rescues Huntington's disease-associated phenotypes.
- Huntingtin-lowering strategies for Huntington's disease.
- Longitudinal Magnetic Resonance Spectroscopy and Diffusion Tensor Imaging in Sheep (Ovis aries) With Quinolinic Acid Lesions of the Striatum: Time-Dependent Recovery of N-Acetylaspartate and Fractional Anisotropy.
- Frequency of the loss of CAA interruption in the HTT CAG tract and implications for Huntington disease in the reduced penetrance range.
- Synergistic activation of AMPK prevents from polyglutamine-induced toxicity in Caenorhabditis elegans.
- Impact of circadian and diurnal rhythms on cellular metabolic function and neurodegenerative diseases.
- Myricetin bioactive effects: moving from preclinical evidence to potential clinical applications.
- Incidence and prevalence of Huntington disease (HD) in the Sultanate of Oman: the first Middle East post-HTT service-based study.
- Synaptic RTP801 contributes to motor-learning dysfunction in Huntington's disease.
- Circadian alterations in patients with neurodegenerative diseases: Neuropathological basis of underlying network mechanisms.
- CRISPR/Cas9 novel therapeutic road for the treatment of neurodegenerative diseases.
- Nascent mutant Huntingtin exon 1 chains do not stall on ribosomes during translation but aggregates do recruit machinery involved in ribosome quality control and RNA.
- Gender Differences in Non-sex Linked Disorders: Insights From Huntington's Disease.
- The Role of Neurovascular System in Neurodegenerative Diseases.
- Effects of high-intensity interval training on gut microbiota profiles in 12 months' old ICR mice.
- Effects of rosmarinic acid on nervous system disorders: an updated review.
- Gene Therapy and immunotherapy as promising strategies to combat Huntington's Disease associated neurodegeneration: Emphasis on recent updates and future perspectives.
- Mammalian Target of Rapamycin-RhoA Signaling Impairments in Direct Striatal Projection Neurons Induce Altered Behaviors and Striatal Physiology in Mice.
- Somatic mutations in neurodegeneration: An update.
- Alzheimer's Disease, Inflammation, and the Role of Antioxidants.
- Clinical, neuropathological, and genetic characterization of STUB1 variants in cerebellar ataxias: a frequent cause of predominant cognitive impairment.
- Antioxidant and Anti-inflammatory Effect of Nrf2 Inducer Dimethyl Fumarate in Neurodegenerative Diseases.
- Correction: Shedding a new light on Huntington's disease: how blood can both propagate and ameliorate disease pathology.
- Therapeutic Update on Huntington's Disease: Symptomatic Treatments and Emerging Disease-Modifying Therapies.
- MAP KINASE SIGNALING AS THERAPEUTIC TARGET FOR NEURODEGENERATION.
- POSCAbilities: The Application of the Prion Organotypic Slice Culture Assay to Neurodegenerative Disease Research.
- Lentiviral delivery of human erythropoietin attenuates hippocampal atrophy and improves cognition in the R6/2 mouse model of Huntington's disease.
- Huntington's disease in Bangladesh.
- Standardized data structures in rare diseases: CDISC user guides for Duchenne muscular dystrophy and Huntington's disease.
- Whether, when, and how to communicate genetic risk to minors: 'I wanted more information but I think they were scared I couldn't handle it'.
- Optical coherence tomography angiography findings in Huntington's disease.
- Drug-Resistant Epilepsy in Children with Juvenile Huntington's Disease: A Challenging Case and Brief Review.
- The functions and mechanisms of prefoldin complex and prefoldin-subunits.
- Artificial miRNAs targeting CAG repeat expansion in ORFs cause rapid deadenylation and translation inhibition of mutant transcripts.
- Phytocannabinoids: General Aspects and Pharmacological Potential in Neurodegenerative Diseases.
- The effects of multidisciplinary rehabilitation on neuroimaging, biological, cognitive and motor outcomes in individuals with premanifest Huntington's disease.
- The Diverse Role of Optineurin in Pathogenesis of Disease.
- Clinical Outcomes and Selection Criteria for Prodromal Huntington's Disease Trials.
- Addendum: American College of Medical Genetics and Genomics Standards and Guidelines for Clinical Genetics Laboratories, 2014 edition: technical standards and guidelines for Huntington disease.
- The longevity-associated variant of BPIFB4 improves a CXCR4-mediated striatum-microglia crosstalk preventing disease progression in a mouse model of Huntington's disease.
- Cell Type-Specific Transcriptomics Reveals that Mutant Huntingtin Leads to Mitochondrial RNA Release and Neuronal Innate Immune Activation.
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