- Metabolic deregulation associated with aging modulates protein aggregation in the yeast model of Huntington's disease
- Structural Mechanisms for VMAT2 inhibition by tetrabenazine
- <em>Huntingtin</em> CAG-expansion mutation results in a dominant negative effect
- Comparison of Huntington's disease phenotype progression in male and female heterozygous FDNQ175 mice
- Oxytosis/Ferroptosis in Neurodegeneration: the Underlying Role of Master Regulator Glutathione Peroxidase 4 (GPX4)
- Harnessing role of sesamol and its nanoformulations against neurodegenerative diseases
- Corrigendum to "Understanding the role of the hematopoietic niche in Huntington's disease's phenotypic expression: In vivo evidence using a parabiosis model" [Neurobiol Dis. 2023 May;180:106091. doi:10.1016/j.nbd.2023.106091. Epub 2023 Mar 24]
- Biosynthesis of neuroprotective melatonin is dysregulated in Huntington's disease
- An Unusual Presentation of Serotonin Syndrome and Subsequent Catatonia in a Patient With a Family History of Huntington's Disease
- Oculomotor Abnormalities in a Sheep (Ovis aries) Model of Huntington's Disease: Towards a Biomarker for Assessing Therapeutic Efficacy
- The temporal event-based model: Learning event timelines in progressive diseases
- Altered Adipocyte Cell Size Distribution Prior to Weight Loss in the R6/2 Model of Huntington's Disease
- ABHD6 Inhibition Rescues a Sex-Dependent Deficit in Motor Coordination in The HdhQ200/200 Mouse Model of Huntington's Disease
- Adaptive HD-sEMG decomposition: Towards robust real-time decoding of neural drive
- Aberrant splicing of mutant huntingtin in Huntington's disease knock-in pigs
- Total recall: the role of PIDDosome components in neurodegeneration
- Identification and Optimization of RNA-Splicing Modulators as Huntingtin Protein-Lowering Agents for the Treatment of Huntington's Disease
- Therapeutic potential of lithium chloride and valproic acid against neuronopathic types of mucopolysaccharidoses through induction of the autophagy process
- A cyclic pyrrole-imidazole polyamide reduces pathogenic RNA in CAG/CTG triplet repeat neurological disease models
- The Dosing of Mobile-Based Just-in-Time Adaptive Self-Management Prompts for Caregivers: Preliminary Findings From a Pilot Microrandomized Study
- Unraveling Huntington's Disease: A Report on Genetic Testing, Clinical Presentation, and Disease Progression
- Guided self-help for anxiety among Huntington's disease gene expansion carriers (GUIDE-HD) compared to treatment as usual: a randomised controlled feasibility trial
- Characterization of structural changes occurring in insulin at different time intervals at room temperature by surface-enhanced Raman spectroscopy
- A clinical study and future prospects for bioactive compounds and semi-synthetic molecules in the therapies for Huntington's disease
- Multi-OMIC analysis of Huntington disease reveals a neuroprotective astrocyte state
- Research progress on the role of extracellular vesicles in neurodegenerative diseases
- The relationship between disease-specific psychosocial stressors and depressive symptoms in Huntington's disease
- Age-Dependent Increase in Tau Phosphorylation at Serine 396 in Huntington's Disease Prefrontal Cortex
- Caregiver burden of patients with Huntington's disease in South Korea
- The enduring enigma of sporadic chorea: A single center case series
- Neurodegenerative disease: New hopes and perspectives
- Nuclear orphan receptors: A novel therapeutic agent in neuroinflammation
- Therapeutic implications of phosphorylation- and dephosphorylation-dependent factors of cAMP-response element-binding protein (CREB) in neurodegeneration
- Mitochondrial dysfunction in neurodegenerative disorders: Potential therapeutic application of mitochondrial transfer to central nervous system-residing cells
- Huntingtin Interacting Proteins and Pathological Implications
- A Specific Mini-Intrabody Mediates Lysosome Degradation of Mutant Huntingtin
- Brain-Derived 11S Regulator (PA28αβ) Promotes Proteasomal Hydrolysis of Elongated Oligoglutamine-Containing Peptides
- Association of Selenium Levels with Neurodegenerative Disease: A Systemic Review and Meta-Analysis
- Huntingtin loss in hepatocytes is associated with altered metabolism, adhesion, and liver zonation
- Development of a cellular reporter assay to measure activity of MutSβ, a therapeutic target for Huntington's disease
- Increase in brain glycogen levels ameliorates disease phenotype and rescues neurodegeneration in the Drosophila model of Huntington's disease
- Neurodegenerative disease-associated inclusion bodies are cleared by selective autophagy in budding yeast
- Shared Molecular Pathways in Glaucoma and Other Neurodegenerative Diseases: Insights from RNA-Seq Analysis and miRNA Regulation for Promising Therapeutic Avenues
- Artificial intelligence in the diagnosis of glaucoma and neurodegenerative diseases
- Detection of Unfolded Cellular Proteins Using Nanochannel Array with Probe-Functionalized Outer-Surfaces
- Activin A targets extrasynaptic NMDA receptors to improve neuronal and behavioral deficits in a mouse model of Huntington disease
- Phosphoproteomics implicates glutamatergic and dopaminergic signalling in the antidepressant-like properties of the iron chelator deferiprone
- Huntingtin Plays a Role in the Physiological Response to Ethanol in Drosophila
- Altered exocytosis of inhibitory synaptic vesicles at single presynaptic terminals of cultured striatal neurons in a knock-in mouse model of Huntington's disease
- Levels of Synaptic Proteins in Brain and Neurofilament Light Chain in Cerebrospinal Fluid and Plasma of OVT73 Huntington's Disease Sheep Support a Prodromal Disease State
- Curcumin, inflammation, and neurological disorders: How are they linked?
- Purtscher-like retinopathy in patients with COVID-19
- Limitations of dual-sgRNA CRISPR strategies for the treatment of CNS genetic disorders
- Nanovesicular-Mediated Intranasal Drug Therapy for Neurodegenerative Disease
- Glutamine stimulates the S6K/4E-BP branch of insulin signalling pathway to mitigate human poly(Q) disorders in <em>Drosophila</em> disease models
- Editorial: The role of posttranslational modifications in polyglutamine diseases
- Generation of two human iPSC lines from dermal fibroblasts of adult- and juvenile-onset Huntington's disease patients and two healthy donors
- Pearls & Oy-sters: Epilepsy is a key feature of pediatric-onset Huntington's disease
- Microprobes for Label-Free Detection of Short Tandem Repeats: An Insight into Alleviating Secondary Structure Effects
- Locomotor Behavior and Memory Dysfunction Induced by 3-Nitropropionic Acid in Adult Zebrafish: Modulation of Dopaminergic Signaling
- Recombinant Antibody Fragments for Neurological Disorders: An Update
- Site-specific acetylation of polynucleotide kinase 3'-phosphatase (PNKP) regulates its distinct role in DNA repair pathways
- The translational potential of cholesterol-based therapies for neurological disease
- Polyglutamine disease in peripheral tissues
- The microRNAs (miRs) overexpressing mesenchymal stem cells (MSCs) therapy in neurological disorders; hope or hype
- The Emerging Role of Sigma Receptors in Pain Medicine
- Disruptive mutations in the serotonin transporter associate serotonin dysfunction with treatment-resistant affective disorder
- Huntingtin bundles and changes the local proteome of actin filaments in neurons
- Oculomotor Apraxia as an Early Presenting Sign of Juvenile-Onset Huntington's Disease
- Rhes depletion promotes striatal accumulation and aggregation of mutant huntingtin in a presymptomatic HD mouse model
- Pharmacological Co-Activation of TrkB and TrkC Receptor Signaling Ameliorates Striatal Neuropathology and Motor Deficits in Mouse Models of Huntington's Disease
- CRISPR/Cas9 genome editing for neurodegenerative diseases
- Sex differences in the pleiotropy of hearing difficulty with imaging-derived phenotypes: a brain-wide investigation.
- Toxic effects of mutant huntingtin in axons are mediated by its proline-rich domain
- The risk of criminal behavior in the elderly and patients with neurodegenerative disease
- From Pathogenesis to Therapeutics: A Review of 150 Years of Huntington's Disease Research
- Brain-Derived Neurotrophic Factor Dysregulation as an Essential Pathological Feature in Huntington's Disease: Mechanisms and Potential Therapeutics
- Beyond Motor Deficits: Environmental Enrichment Mitigates Huntington's Disease Effects in YAC128 Mice
- Mitochondrial Dysfunction in Repeat Expansion Diseases
- Mesenchymal Stem Cell-Derived Extracellular Vesicles: An Emerging Diagnostic and Therapeutic Biomolecules for Neurodegenerative Disabilities
- The Disruption of NMDAR/TRPM4 Death Signaling with TwinF Interface Inhibitors: A New Pharmacological Principle for Neuroprotection
- The Role of Hydrogen Sulfide (H<sub>2</sub>S) in Epigenetic Regulation of Neurodegenerative Diseases: A Systematic Review
- The Urine Metabolome of R6/2 and zQ175DN Huntington's Disease Mouse Models
- Research on Ferroptosis as a Therapeutic Target for the Treatment of Neurodegenerative Diseases
- Four octapeptide repeat insertion (4-OPRI) in <em>PRNP</em> causing Huntington disease phenocopy
- Meningeal T cells function in the central nervous system homeostasis and neurodegenerative diseases
- Spatiotemporal optical control of Gαq-PLCβ interactions
- Sleep, Circadian Rhythms, and Cognitive Dysfunction in Huntington's Disease
- Skeletal muscle cell protein dysregulation highlights the pathogenesis mechanism of myopathy-associated p97/VCP R155H mutations
- PolyQ Database-an integrated database on polyglutamine diseases
- What Is Huntington Disease?
- Hippocampal morphology in Huntington's disease, implications for plasticity and pathogenesis: The IMAGE-HD study
- Caenorhabditis elegans: A transgenic model for studying age-associated neurodegenerative diseases
- Neural oscillations modulation during working memory in pre-manifest and early Huntington's disease
- Effect of <em>Shorea robusta</em> resin extract in 3-nitropropionic acid-induced Huntington's disease symptoms in Sprague-Dawley rats
- Gelation of cytoplasmic expanded CAG RNA repeats suppresses global protein synthesis
- Incidence and morphology of secondary TDP-43 proteinopathies: Part 2
- Epigallocatechin Gallate: A Multifaceted Molecule for Neurological Disorders and Neurotropic Viral Infections
- Oligodendrocyte pathology in Huntington's disease: from mechanisms to therapeutics
- In Vivo Cerebral Imaging of Mutant Huntingtin Aggregates Using <sup>11</sup>C-CHDI-180R PET in a Nonhuman Primate Model of Huntington Disease
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